PORFIRIAS · u roll vs oro o . mixed copro variegate cutanea-tarda congenital erythropoietic...

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Transcript of PORFIRIAS · u roll vs oro o . mixed copro variegate cutanea-tarda congenital erythropoietic...

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PORFIRIAS

Senador Morán Sánchez

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CONCEPTO

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CLINICA

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CLASIFICACION

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DXO

• METODOS DE CRIBADO

• CUANTITATIVOS

• ENZIMAS

• GENES

Lampara de Wood

•PRECURSORES

•PORFIRINAS FRACCIONADAS

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CLINICA

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PAI

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CLINICA

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PCT

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TRATAMIENTO

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