Hueso y blandos.america
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Transcript of Hueso y blandos.america
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TUMORES OSEOS
CARLOS EVELIO GRISALES GUTIERREZMEDICO PATOLOGO
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TUMORES FORMADORES DE HUESO
OSTEOMA Abultamiento óseo redondo u oval =Subperiostico: Cráneo o cara, solitarios,
mediana edad y benignos. =Múltiples: Síndrome de Gardner
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TUMORES FORMADORES DE HUESO
OSTEOMA OSTIODE• Son menores de 2 cms, entre los 10 m y 30
años, relación varón mujer 2 a 1, dolorosos por aumento de la prostaglandina E2, cede a la aspirina.
OSTEOBLASTOMA• Columna, dolor intenso
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osteoma
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osteoma
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osteoma
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OSTEOSARCOMA
• Tumor mesenquimatoso maligno cuyas células neoplásicas malignas producen matriz ósea.
• Es el mas frecuente de los malignos óseos• El 75% son menores de 20 años• Relación hombre mujer 1.6:1• Región metafisiaria de huesos largos• Se asocia al Retinoblastoma hereditario
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MORFOLOGIA
• Voluminosos, blando grisáceo• Áreas hemorrágicas y degeneración quística• Destruyen la cortical• Diseminan por la cavidad medular• Con cartílago, osteosarcoma condroblastico
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osteosarcoma
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osteosarcoma
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osteosarcoma
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EVOLUCION CLINICA
• FRACTURA ESPONTANEA• INVASION DE VASOS SANGUINEOS• CUANDO SE HACE Dx 20% TIENEN
METASTASIS A PULMON LUEGO A HUESOS, CEREBRO, ETC
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RADIOGRAFIA Y TRATAMIENTO
• GRAN MASA DESTRUCTIVA, LITICA Y BLASTICA
• LEVANTA EL PERIOSTIO (TRIANGULO DE CODMAN)
• QUIMIOTERAPIA Y AMPUTACION• PRONOSTICO DE 60% CON DIAGNOSTICO
A TIEMPO
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osteosarcoma
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osteosarcoma
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TUMORES FORMADORES DE CARTILAGO
Forman cartílago hialino, mixoide, elástico y fibroconectivo.
OSTEOCONDROMA Exocistosis proliferativa tapizada de cartílago
unida al hueso subyacente por pedículo óseo, solitario o múltiple.
Hombre mujer 3:1, cerca a rodilla, pelvis, 1 a 20 cms, dolorosas
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osteocondroma
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CONDROMAS
• Pueden formarse en la cavidad medular o subperiostico.• Mas frecuente en pies y manos, 20 a
50 años, menor de 3 cms, asintomáticos• Enfermedad de Ollier si múltiples• Síndrome de Maffuci si
hemangiomas de tejidos blandos
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condroma
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CONDROSARCOMA
SON INTRAMEDULARES Y YUXTACORTICALES
CLASIFICACION HISTOLOGICA• Convencional (hialino y/o mixoide)• Células claras• Indiferenciado• Mesenquimatoso
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CONDROSARCOMA
• Mayores de 40 años, hombre mujer 2 a 1• Pelvis, hombros, costillas• Masa dolorosa de 10 cms• Pronostico a 5 años del 90% en grado 1 y
43% en grado 3 con metástasis en 70% a pulmón y huesos
• Tratamiento extirpación y quimioterapia
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condrosarcoma
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condrosarcoma
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condrosarcoma
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Fibroma osificante
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DISPLASIA FIBROSA
Lesión seudotumoral benigna del hueso que se caracteriza por una detención localizada del desarrollo; están presentes todos los elementos del hueso normal, pero no se han diferenciado en estructuras maduras
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DISPLASIA FIBROSA
FORMAS CLINICAS
• MONOSTOTICA, afecta un solo hueso• POLIOSTOTICA, afecta muchos huesos• ENFERMEDAD POLIOSTOTICA, que se
asocia a manchas de piel color café con leche y trastornos endocrinos, pubertad precoz
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DISPLASIA FIBROSA MONOSTOTICA
• 70% DE LAS DISPLASIAS• IGUAL HOMBRE MUJER,
ADOLESCENCIA• LOCALIZAN EN COSTILLAS, FEMUR,
TIBIA, MANDIBULA, CRANEO, HUMERO
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Displasia fibrosa monostotica
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Displasia fibrosa monostotica
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Displasia fibrosa
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DISPLASIA FIBROSA POLIOSTOTICA
• 27% DE LAS DISPLASIAS• ADOLESCENCIA• FEMUR, CRANEO, TIBIA, HUMERO,
COSTILLAS, PERONE, RADIO, CUBITO, MANDIBULA, VERTEBRAS
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Displasia fibrosa
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Displasia fibrosa
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Displasia fibrosa
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ENFERMEDAD POLIOSTOTICA
• SINDROME DE McCUNE ALBRIGHT, 3%• ALTERACION SOMATICA (NO HEREDITARIA)
DE LA EMBRIOGENESIS CON PRECOCIDAD SEXUAL, HIPERTIROIDISMO, ADENOMAS HIPOFISIARIOS CON AUMENTO DE LA HORMONA DE CRECIMIENTO, HIPERPLASIA SUPRARRENAL PRIMARIA
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SARCOMA DE EWING
CELULAS REDONDAS PEQUEÑAS (NEURAL)• 6 a 10% de tumores óseos malignos• 10 a 15 años de edad, algo mayor en hombres• Cavidad medular e invaden cortical y periostio• Diáfisis de huesos largos, fémur, huesos planos
como pelvis, masa dolorosa• Tratamiento quirúrgico y quimioterapia• Pronostico 75% a 5 años
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Sarcoma de Ewing
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Sarcoma de Ewing
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Sarcoma de Ewing
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TUMOR DE CELULAS GIGANTES
• De células gigantes tipo osteoclastos, multinucleados.
• Raro, benigno pero agresivo localmente• Entre los 20 y 50 años• Afectan epífisis y metafisis, mayoría
rodilla• Tto: legrado con recidivas en 40 a 60%
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Tumor de células gigantes
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Tumor de células gigantes
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Tumor de células gigantes
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METASTASIS OSEAS
DISEMINACION
• 1. PROPAGACION DIRECTA• 2. LINFATICA O VASCULAR• 3. INTRARAQUIDEA
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METASTASIS
• Huesos mas comprometidos columna, pelvis, costillas, cráneo, esternón, fémur y humero• La mayoría proviene de próstata, mama,
riñón y pulmón• Metástasis única entonces tiroides y
riñón
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METASTASIS
• EN NIÑOS PROVIENEN DE NEUROBLASTOMA, TUMOR DE WILMS, OSTEOSARCOMAS, SARCOMA DE EWING, RABDOMIOSARCOMA
• HUESOS DE MANOS Y PIES, PROVIENEN DE PULMON, RIÑON Y COLON
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Metástasis hepática
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Carcinoma metástasis
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TUMORES DE TEJIDOS BLANDOS
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GENERALIDADES
LOCALIZACION
• 40% EN MIEMBROS INFERIORES• 30% TRONCO Y REGION RETROPERITONEAL• 20% EN MIEMBROS SUPERIORES• 10% EN CABEZA Y CUELLO
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SARCOMAS
• RELACION HOMBRE MUJER 1.4:1• 15% APARECEN EN NIÑOS• RABDOMIOSARCOMAS EN NIÑOS• SARCOMA SINOVIAL EN ADULTOS JOVENES• LIPOSARCOMA E HISTIOSARCOMA EN
ADULTOS
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PRONOSTICO
• De acuerdo al grado de diferenciación• Numero de mitosis por campo• Pleomorfismo celular• Necrosis• Tamaño y profundidad
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PRONOSTICO
• ALTO GRADO Y PROFUNDO: METASTASIS EN 80% SI ES MAYOR DE 20 CMS
40% SI ES MAYOR A 5 CMS• EN GENERAL LA SUPERVIVENCIA DE LOS
SARCOMAS A LOS 10 AÑOS ES DEL 40%
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LIPOMAS
TUMOR MAS FRECUENTE EN ADULTOS SE CLASIFICAN POR SU MORFOLOGIA EN: 1. CONVENCIONAL 2. FIBROLIPOMA 3. ANGIOLIPOMA 4. DE CELULAS FUSIFORMES 5. MIELOLIPOMA 6. PLEOMORFICO
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lipoma
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lipoma
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lipoma
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LIPOSARCOMA
ADULTOS ENTRE QUINTO Y SEPTIMO DECENIO LOCALIZAN EN REGION PROXIMAL DE
MIEMBROS Y RETROPERITONEAL• CLASIFICAN EN:• 1. mixoides• 2. células redondas• 3. pleomorfico
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liposarcoma
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liposarcoma
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TUMORES Y LESIONES PSEUDOTUMORALES DEL TEJIDO FIBROSO
• PROLIFERACIONES PSEUDOSARCOMATOSAS REACTIVAS POR TRAUMAS LOCALIZADOS, POR ISQUEMIA O ACTIVIDADES DEPORTIVAS
• APARECEN SUBITAMENTE Y CRECEN RAPIDAMENTE
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FIBROSARCOMA
• LOCALIZACION RETROPERITONEAL, MUSLO, RODILLA Y DISTAL DE MIEMBROS
• MASAS BLANDAS CON ASPECTO DE CARNE DE PESCADO
• RECIDIVAN EN MAS DEL 50%• METASTASIS EN EL 25%
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fibrosarcoma
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fibrosarcoma
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TUMORES FIBROHISTIOCITARIOS
HISTIOCITOMA FIBROSO BENIGNO
• Nacen en dermis y tejido celular subcutáneo• Nódulo indoloro de un cm
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Histiocitoma fibroso benigno
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Histiocitoma fibroso benigno
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Histiocitoma fibroso maligno
Proximal de miembros y retroperitoneal Recidiva y metastatizan el 30 a 50% VARIEDADES: 1. Pleomorfico arremolinado 2. Mixoide 3. Inflamatorio 4. Células gigantes 5. Angiomatoide
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Histiocitoma fibroso maligno
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TUMORES DEL MUSCULO ESQUELETICO
RABDOMIOSARCOMA FRECUENTE EN INFANCIA Y ADOLESCENCIA CABEZA Y CUELLO, GENITOURINARIO VARIEDADES: 1. EMBRIONARIO, 66% 2. ALVEOLAR, MUSCULATURA DE MIEMBROS 3. PLEOMORFICO
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rabdomiosarcoma
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rabdomiosarcoma
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LEIOMIOMA
LOCALIZAN EN UTERO, PIEL, GENITALES, TEJIDO SUBCUTANEO, TUBO DIGESTIVO
LEIOMIOSARCOMA• 10-20% DE LOS SARCOMAS,• ADULTOS, MUJERES• LOCALIZAN PIEL, TEJIDO BLANDO PROFUNDO
DE MIEMBROS Y RETROPERITONEO
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leiomiosarcoma
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leiomiosarcoma
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