12 ANOMALÃAS DEL SISTEMA NERVIOSO CENTRAL
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ANOMALÍAS DEL SISTEMNERVIOSO CENTRAL
Dolka Marin Dávalos Joseyn Mejía Mimbela
Alisson Mejia Sánchez
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TUBO NEUA!
•
S"N"#"
$ semana como %lacane&ral %or 'elan(e 'el n)'&lo%rimi(ivo
• los bor'es se elevaran y*ormaran los %lie+&es ne&rales
• ,lie+&es se elevan mas y se
a%ro-iman en(re si en líneame'ia *&sionán'ose y*orman'o el TUBO NEUA!
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*&si)n 'e los%lie+&es
ne&rales
• .&si)n comienzaen re+i)n cervicaly con(in&a en'irecci)n ce*álicao ca&'al
•
Se *orman losne&ro%oroscraneal y ca&'al
• El cierre 'e/ni(ivo'el ne&ro%orocraneal se %ro'&ceen el es(a'io 'e01 a 23 somi(as
4a los 25 'ías6• Ne&ro%oro ca&'al
se obli(era &nos'ías 'es%&7s"
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El e-(remo ce*álico 'el (&bo ne&ral se 'ily ori+ina $ vesíc&las ence*álicas %rimaria
an(erior
%os(eri
or
• ,rosence*alo ) cerebro
an(erior• Mesence*alo ) cerebro
me'io• ombence*alo ) cerebro
%os(erior
Me'&laes%inal
.le-&ra cervical
m e ' i o
.le-&ras• .le-&ra cervical"= en(re
me'&la y cerebro %os(erior•
.le-&ra ce*álica "= en la&ni)n 'el mesence*alo
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!as c7l&las 'e las cres(as ne&rales *orman las 'os menin+esin(ernas> la aracnoi'es y %iama're9 la '&rama're es *orma'a'e Mes7n8&ima"
El canal cen(ral se e-(ien'e a la lon+i(&' 'e la m7'&la es%inal'&ran(e el 'esarrollo" Es(a ro'ea'o %or c7l&las e%en'imarias ylleno 'e lí8&i'o ce*alorra8&í'eo9 con(in&án'ose con el c&ar(oven(ríc&lo en la %ar(e baja 'e el (allo cerebral" En a'&l(os9 elcanal &s&almen(e 'esa%arece e-ce%(o a nivel cervical"
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Enc7*alos(r&c(&ras ence*álicas a%arecen l&e+o 'e oc&rri'os ; %rocesos básicos
,roli*eracion ne&ralMi+racion
,erio'o 'eor+anizaci)nmielinizacion
• TELENCEFALO 2 eva+inaciones
la(eraleshemisferios
!"er!es#rimi"i$os
• DIENCEFALOeva+inaci)n 'e
las vesíc&las)%(icas
Se se%ara 'elrombence*alo %or&n s&rco %ro*&n'o
?el i(smo 'elrombence*alo@
• MET*
%ro(e
• MIE el *
Em%ri&' ( sem!'!s
PROMENSENCEFALO MESENCEFALO ROMB
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El lími(e me(enc7*alo=mielenc7*alo 8&e'a'e/ni'o %or el %lie+&e %ro(&berancial"Es(e %lie+&e se ori+ina 'ebi'o al
crecimien(o 'esi+&al 'el rombenc7*alo'an'o l&+ar a &n a'el+azamien(o 'e s&(echo"Al %rinci%io9 el enc7*alo (iene s&es(r&c(&ra básica m&y similar a lam7'&la es%inal9 sin embar+o9 'ebi'o a laa%arici)n 'e los %lie+&es y s&rcosence*álicos se %ro'&cen variacionesconsi'erables en la 'is%osici)n 'e los'i*eren(es elemen(os" En +eneral9 las%lacas alares y basales 'el rombenc7*aloy mesenc7*alo se enc&en(ran bien'e/ni'as9 en cambio9 en el %rosenc7*alolas %lacas alares es(án acen(&a'as y lasbasales en %lena re+resi)n"
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MALFORMACIO
NES DELSISTEMA
NERVIOSO
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FACTORES AMBIENTALES
Me'ioAmbien(e
Alcohol
Desechos T)-icos
i%er(ermia y Es(a'os
.ebriles
a'iaci)n9Me(ilmerc&rio y ,lomo
Escocia yales
#hina9E+i%(o eGn'ia
A l ( a
i n c i ' e n c i a
•
•
•
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FACTORES AMBIENTALES
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FACTORES AMBIENTALESA+&a
'e
beber"03
m+H!
De/ciencia 'en&(rien(es
S&%eriores a los• e(ar'o
• MicroceMenor %ro%
car'io%a(ías9 recrecimien(o y
es%on(án
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FACTORES AMBIENTALES
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FACTORES MULTIFACTORIALE
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FACTORES MULTIFACTORIALE
Á*i+o f&i*o Co%!!mi'! -B./0
• #o*ac(ores en la conversi)n 'e lahemocis(eína a me(ionina9 'a &nincremen(o 'e la hemocis(eína Anomalías SN#
• M&(aci)n 'el +en %ara la acci)n 'ela me(ilen(e(rahi'ro*ola(o
re'&c(asa o &n 'e*ec(o 'e lame(ionina sin(e(asa9 habien'o &naal(eraci)n> Del me(abolismo 'el *ola(o En la sín(esis 'e los
n&cle)(i'os De las conversiones 'e los
aminoáci'os
Vi"!mi'!s• Análo+os 'e la vi(amina A
4Gso(re(inoína6 'a l&+ar a &embrio%a(ía %or áci'o re(in Al(eraciones 'el SN#9
craneo*aciales y car'i
• El *ármaco e(re(ina(o 4'eriv
vi(amina A6 %osee &na vi'a%rolon+a'a 'e has(a (res a'es%&7s 'e in(err&m%ir s&a'minis(raci)n Gn'is%ensable (ra(ami
an(iconce%cional e/cam&jeres 8&e lo &san"
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MALFORMACIONES DEL
ENCÉFALO
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MENIN)OENCEFALOCELE
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MENIN)OCELE
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MENIN)OCELEDi!1
"r
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ANENCEFALIA
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MICROCEFALIA
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MACROCEFALIA
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#AUSAS
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2IDROCEFALIA
, '
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,&e'e ser>
MALFORMACIO
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MALFORMACIO
NES DE LAMÉDULA
ESPINAL
Í
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ESPINA BÍFIDA
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MENIN)OCELE
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MIELOMENIN)OCELE• Es &n 'e*ec(o 'el (&bo
ne&ral como res&l(a'o 'ela herniaci)n o sac&laci)n'e las menin+es y 'e lam7'&la es%inal a (rav7s'e la *alla 'el cierre 'elarco y lámina ver(ebral
%resen(án'ose conmayor *rec&encia en lare+i)n l&mbosacra"
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MIELOS4UISIS
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MIELOS4UISIS
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